Product Detail
Product NameSGSH antibody
Host SpeciesRabbit
ClonalityPolyclonal
PurificationAffinity purified by Protein A.
ApplicationsWB
Species ReactivityHu
Immunogen TypeRecombinant protein
Immunogen DescRecombinant protein fragment contain a sequence corresponding to a region within amino acids 44 and 200 of Human SGSH
Target NameSGSH
ConjugateUnconjugated
Accession NoSwiss-Prot:P51688
Gene ID:6448
Uniprot
P51688
Gene ID
6448;
Concentration2mg/ml
FormulationSupplied in 0.1M Tris-buffered saline with 10% Glycerol (pH7.0). 0.01% Thimerosal was added as a preservative.
StorageStore at -20˚C for long term preservation (recommended). Store at 4˚C for short term use.
Application Details
Predicted MW: 57kd
Western blotting: 1:500-1:3000
Sample (30 ug of whole cell lysate)
A: 293T
7.5% SDS PAGE
Primary antibody diluted at 1: 1000
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq]
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